CF affects many organs, primarily the lungs and those responsible for digestion. In CF there is a problem with the protein that controls the movement of salt and water in and out of the cells. Salt plays an important part in thinning out mucus in the body. Due to a lack of salt in the cells of someone with CF, mucus becomes thick and sticky. It then builds up in organs, including the lungs and pancreas. This mucus clogs the tiny air passages in the lungs and traps bacteria. Repeated infections and blockages can cause irreversible lung damage and death.
Thanks to ongoing research and improved treatments, the life expectancy for someone living with Cystic Fibrosis today is around 54 years. Outcomes still vary considerably between individuals, but tragically, more than half of those with CF do not live to the age of 30.
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